Abstract. Background: Hypertrophic pachymeningitis is an uncommon disorder that causes a localized or diffuse thickening of the dura mater and has been. Summary: Idiopathic hypertrophic cranial pachymeningitis is a rare inflammatory disease with diffused involvement of the dura. Often, the definite diagnosis is. Hypertrophic pachymeningitis is a unique clinical entity characterised by fibrosis and thickening of the duramater with resulting neurological dysfunction.

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Churchill livingstone ; New York.

Hypertrophic pachymeningitis | Radiology Reference Article |

MR imaging of the meninges. The relationship of idiopathic hypertrophic pachymeningitis with connective tissue disease or vasculitis syndrome is discussed. This article has been cited by other articles in PMC. Inflammatory hypertrophic cranial pachymeningitis.

How to cite this URL: Imaging appearance of pachymeningeal tuberculosis. Optic neuropathy associated with hypertrophic cranial pachymeningitis. Discussion Hypertrophic pachymeningitis is a rare disorder of diverse etiology.

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Microscopic examination of the dura showed dense fibrosis with inflammatory cell infiltration composed mainly of lymphocytes.

Edit article Share article View revision history. Enhanced MR imaging of hypertrophic pachymeningitis.

The clinical course was chronic. Idiopathic hypertrophic cranial pachymeningitis: Eur J Radiol ; Related Radiopaedia articles Infections of the central nervous system CNS infections classification by etiology viral eastern equine encephalitis enterovirus rhomboencephalitis flavivirus encephalitis Japanese encephalitis West Nile fever Murray Valley encephalitis St. About Blog Go ad-free.

Hypertrophic pachymeningitis

BhanuSakthi Velayuthamand M. A study of seven cases. Gadolinium-enhanced T1-weighted MR images show marked enhancement of the dural edges. It was first described by Charcot and later by Naffziger and Stern.

Ann Indian Acad Neurol. His past history was not contributory. Case 1 Case 1. All patients were treated with corticosteroid and improved intially, but pacyhmeningitis of them experienced relapses.

How to cite this article: Idiopathic hypertrophic pachymeningeal lesions: Report of a case and review of literature. Introduction Hypertrophic pachymeningitis is a rare form of diffuse inflammatory disease that causes thickening of the dura mater.


Case records of the Massachusetts general hospital. Long term improvement of idiopathic hypertrophic cranial pachymeningitis by lymphocytapheresis. Four patients underwent biopsy of the dura, and the pathological study showed non-specific inflammatory changes.

Hypertrophic pachymeningitis

Case 2 Case 2. Hypertrophic pachymeningitis is a rare disorder of diverse etiology. J Neurol Neurosurg Psychiatry ; Please review our privacy policy. Two patients received surgical intervention.

Idiopathic hypertrophic pachymeningitis.

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