Dyke-Davidoff-Masson syndrome is characterized by unilateral atrophy of cerebral hemispheres, enlargement of the ipsilateral sulci, ventricles, and cisternal sp. Dyke-Davidoff-Masson syndrome is a rare condition of unknown frequency resulting from brain injury due to a multitude of causes; especially in. Dyke-Davidoff-Masson Syndrome (DDMS) refers to atrophy or hypoplasia of one cerebral hemisphere. (hemiatrophy) which is secondary to brain insult.

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Dyke-Davidoff-Masson syndrome

There was also shift of midline to left and thickening of calvarium on the left side [ Figure 1 ]. Yerdelen D, Zafer F. Sign in to save your search Sign in to your personal account. Articles Cases Courses Quiz. Log in Sign up. Mazson patient did not attend school.

Dyke-Davidoff-Masson syndrome | Radiology Reference Article |

Create a free personal account to download free article PDFs, sign up for alerts, customize your interests, and more. Support Radiopaedia and see fewer ads. Clinical presentation Radiographic features History and etymology Differential diagnosis References Images: Graham A, Molnar Z.

Synonyms or Alternate Spellings: It has been reported that DDMS is caused by cerebral insult that may occur in utero when the maturation of calvarium has not been completed, or during early life due to brain damage usually traumatic.


On examination, the child had very poor cognitive function and was undernourished. National Center for Biotechnology InformationU.

Cerebral hemiatrophy can be of two types, infantile congenital and acquired. The patients have seizure disorder, mental retardation, and hemiparesis. Computed tomography in cerebral hemiatrophy. Check dafidoff errors and try again. Journal List J Pediatr Neurosci v.

A plain and contrast CT of the brain was done which revealed atrophy of left cerebral hemisphere with dilatation of the ipsilateral ventricle, widening of sulci and sylvian fissure on the same side. Positive findings were — microcephaly — severe mental retardation with an intelligence quotient of 40, right-sided facial palsy, and mazson gap in both the lower limbs.

Sturge-Weber syndrome Sturge-Weber syndrome. Birth history was uneventful. We present a case massoon Dyke Davidoff-Masson-syndrome dyje typical clinical and imaging features. Sometimes multiple anticonvulsants are in use. A rare neurocutaneous syndrome. Discussion InDyke, Davidoff and Masson first described the syndrome in plain radiographic and pneumoencephalographic changes in a series of nine patients. Patients with DDMS usually present with refractory seizures and the treatment should focus on control of the seizures with suitable anticonvulsants.

Dyke-Davidoff-Masson syndrome

Author information Copyright and License information Disclaimer. The surface of the hemisphere remains smooth and uninterrupted until early in the fourth month of gestation. This feature differentiates it from cerebral hemiatrophy which occurs in early life. Support Center Support Center.


Introduction Dyke—Davidoff—Masson syndrome DDMS is described as skull radiographic and pneumatoencephalographic changes in their series of nine patients whose clinical characteristics included hemiparesis, seizures, facial asymmetry, and mental retardation which was ddavidoff in by Dyke et al.

In some sources, it is equated to hemispheric infarctionwhereas in other sources any cause of cerebral hemiatrophy is included. The imaging features include unilateral hemispheric atrophy without any calvarial changes.

The main causes of acquired type are trauma, tumor, infection, ischemia, hemorrhage, and prolonged febrile seizure. He had delayed milestones of development in the form of not able to stand or walk and not spoken a word. Along with drugs, physiotherapy, occupational therapy, and speech therapy play a significant role in long-term management of the child.

Birth trauma, hypoxia, intracranial hemorrhage, tumors, infections, and prolonged febrile seizures after birth are important peri- and post-natal causes. Case daavidoff Case 1. It usually presents with intractable focal epilepsy and cognitive defects in children. Introduction Dyke-Davidoff-Masson syndrome DDMS refers to atrophy or hypoplasia of one cerebral hemisphere hemiatrophywhich is usually due to an insult to the developing brain in fetal or early childhood period.